Two Cases of Generalized Nonconvulsive Status Epilepticus with Eyelid Myoclonia with Absence

J Korean Neurol Assoc > Volume 24(2); 2006 > Article

Journal of the Korean Neurological Association 2006;24(2): 153-156.

의식결여와 안검 간대성근경련을 동반한 비경련성 간질중첩증 2예

박형준, 이지은 김지윤 박수철

연세대학교 의과대학 신경과학교실

Two Cases of Generalized Nonconvulsive Status Epilepticus with Eyelid Myoclonia with Absence

Hyung Jun Park, M.D.

Departments of Neurology, Yonsei University College of Medicine, Seoul, Korea

Abstract

Eyelid myoclonia with absence is a distinct syndrome of idiopathic generalized epilepsy, characterized by the triad of eyelid myoclonia associated with brief absences, generalized discharges of 3-6 Hz polyspike and slow waves, which are mainly precipitated by eye closure or photosensitivity. We experienced two women with eyelid myoclonia with absence, who typically showed fixation off sensitivity and catatmenial exacerbation. Carabamazepine monotherapy aggravated the seizure frequency and resulted in nonconvulsive status epilepticus. These cases have not previously been reported in Korea.KeyWords:Eyelid myoclonia with absence, Status epilepticus, Fixation off sensitivity