A Case of Bickerstaff's Brainstem Encephalitis with Guillain-Barre Syndrome Presenting Optic Neuropathy and Seizure

J Korean Neurol Assoc > Volume 23(3); 2005 > Article

Journal of the Korean Neurological Association 2005;23(3): 389-391.

길랑-바레증후군이 동반된 Bickerstaff 뇌간뇌염에서 나타난 시신경병증과 경련발작 1예

도영록, 김지언 곽재혁 권오대 도진국 이동국

대구가톨릭대학교 의과대학 신경과학교실

A Case of Bickerstaff's Brainstem Encephalitis with Guillain-Barre Syndrome Presenting Optic Neuropathy and Seizure

Young Rok Do

Department of Neurology, Catholic University of Daegu School of Medicine, Daegu, Korea

Abstract

Bickerstaff's brainstem encephalitis (BBE), characterized by acute ophthalmoplegia and ataxia, often causes impaired consciousness and hyperreflexia. A 17-year-old man was admitted with an acute meningitic condition including high and neck stiffness. His condition rapidly deteriorated over 2 weeks, and he showed ophthalmoplegia, ataxia, seizure, tetraplegia, comatose mentality, and optic neuropathy. Electroencephalography showed diffuse slow waves. Visual evoked potentials showed no responses in the right eye. This is the first case of BBE with Guillain-Barre syndrome presenting with optic neuropathy and seizure. KeyWords:Brain stem encephalitis, Optic neuropathy, Seizures