A Case of Subcortical Heterotopia in Hemiparkinson-Hemiatrophy Syndrome

J Korean Neurol Assoc > Volume 23(2); 2005 > Article

Journal of the Korean Neurological Association 2005;23(2): 274-277.

반파킨슨-반위축 증후군에서 피질하 이형성증을 보인 1예

조현, 백종삼 박재현 김정연 강석윤

인제대학교 의과대학 상계백병원 신경과, 연세대학교 의과대학 신경과학교실

A Case of Subcortical Heterotopia in Hemiparkinson-Hemiatrophy Syndrome

Hyun Cho

Department of Neurology, Inje University College of Medicine, Sanggye Paik Hospital, Seoul; Department of Neurology, Yonsei University College of Medicine*, Seoul, Korea

Abstract

Hemiparkinson-hemiatrophy (HP-HA) syndrome is a rare form of secondary parkinsonism. We present a case of a 19-year-old, left-handed man with subcortical heterotopia. He had hemiatrophy and hemiparkinsonian symptoms on his right side. We described the clinical, neuroradiological and neurophysiologic findings including transcranial magnetic stimulation study. These findings were compatible with HP-HA syndrome and his symptoms were markedly improved with levodopa treatment. KeyWords:Hemiparkinson-hemiatrophy, Heterotopia, Transcranial magnetic stimulation