Intravascular Lymphomatosis Presenting as Demyelinating Disease: A Case Report

J Korean Neurol Assoc > Volume 22(5); 2004 > Article

Journal of the Korean Neurological Association 2004;22(5): 535-538.

탈수초 질환의 양상을 보인 혈관내 림프종증 1예

박현동, 박제원 김승현 김주한 김희태 김명호 장세진

한양대학교 의과대학 신경과학교실, 울산대학교 의과대학 병리학교실*

Intravascular Lymphomatosis Presenting as Demyelinating Disease: A Case Report

Hyun-dong Park

Department of Neurology, Hanyang University College of Medicine, Seoul; Department of Pathology, University of Ulsan College of Medicine*, Seoul, Korea

Abstract

Intravascular lymphomatosis (IL) is known as a rare and fatal disease characterized by massive intravascular proliferations of B or T lymphoid cells and manifests in the nervous system and skin. However diagnosis is usually made at the time of autopsy because of the lack of characteristic clinical or laboratory findings. Therefore, IL may be confused with various forms of neurological diseases including demyelinating disease, encephalitis, vasculitis or stroke. We report a case of post-mortem confirmed IL presenting as demyelinating disease. Key Words: Intravascular lymphomatosis, Demyelinating disease