Two Cases of Unverricht-Lundborg Disease

J Korean Neurol Assoc > Volume 7(1); 1989 > Article

Journal of the Korean Neurological Association 1989;7(1): 157-164.

Unverricht-Lundborg Disease 2례

이상건, 한설희,김병준,노재규,이상복,명호진,김종성

서울대학교 신경과. 서울중앙병원 신경과.

Two Cases of Unverricht-Lundborg Disease

Sang-Kun Lee,M.D., Seol-Heui Han,M.D., Jae-Kyu Rho,M.D., Sang-Bok Lee,M.D., Ho-Jin Myung,M.D.

Department of neurology , College of medicine, Seoul National University Department of neurology , Asan Medical Center

Abstract

Unverricht-Lundborg disease(Baltic myoclonus) is one of the major causes of progressive myoclonus epilepsy. It is characterized by stimulus sensitive myoclonic seizure, generaized tonic-clonic seizure, generally synchronous polyspike and wave discharges on EEG and absence of severe or early dementia. It has usually been described in the countries around the Baltic area. But recently, it is regarded as the most common form of progressive myoclonus epilepsy in the other countries as well. We report, with the review of the literature, two patients who showed the typical features of this disorder,