A Case Report of Progressive Supranuclear Palsy 
(Steele-Richardson-Olszewski Syndrome)

J Korean Neurol Assoc > Volume 2(2); 1984 > Article

Journal of the Korean Neurological Association 1984;2(2): 188-192.

진행성 핵상마비 1예 보고

선우일남, 조필자

연세대학교 신경과. 국립의료원 신경과.

A Case Report of Progressive Supranuclear Palsy (Steele-Richardson-Olszewski Syndrome)

Il-Nam Seonwoo, M.D., Pil-Ja Cho, M.D.

Department of Neurology, Yeonsei University, Department of Neurology National Medical Center

Abstract

Progressive Supranuclear Palsy (PSP) is a rare degenerative disease showing supranuclear ophthalmoplegia, rseudobulbar palsy and several parkinsonian features. This is , as far as the author's knowledge, the first case in this country. The patient is a 55 year old female with slowly progressive disturbances in walking, swallowing, speech and behaviors. The most characteristic finding is the prominent external ophthalmoplegia, especially vertical and downward gaze, which can be easily overcome by the oculocephalic reflexes (Doll's eye movements). The dyspagia, dysarthria and emotional lability may suggest the pseudobulbar palsy. General hyper-reflexia and Babinski sign are noted. There are several features of parkinsonism, but the rigidity is more severe in the trunk than in the extremities and the posture is rather hyperextended than scooped. There is no tremor. The disease is slowly progressive and the medical treatment for Parkinson's disease is not effective.