Primary Angiitis of the Central Nervous System Presenting Tumefactive Lesions and Small Arteriolar Ectasias

J Korean Neurol Assoc > Volume 29(3); 2011 > Article

Journal of the Korean Neurological Association 2011;29(3): 257-260.

종양성 병변과 세동맥 확장 소견을 보인 중추신경계원발혈관염

조방훈, 박은선 김동은 김준태 박만석 김형석a 김가언b 윤 웅c 정 신d 조기현

전남대학교 의과대학 신경과학교실, 뇌혈관센터, 법의학교실a, 병리학교실b, 영상의학교실c, 신경외과학교실d

Primary Angiitis of the Central Nervous System Presenting Tumefactive Lesions and Small Arteriolar Ectasias

Bang-Hoon Cho

Department of Neurology, Cerebrovascular Center, Departments of Forensic Medicinea, Anatomical Pathologyb, Diagnostic Radiologyc, and Neurosurgeryd, Chonnam National University Medical School, Gwangju, Korea

Abstract

Primary angiitis of the central nervous system (PACNS) is a rare disorder of unknown etiology and a serious form of vasculitis that is limited to the brain and spinal cord. We report a case of PACNS presenting with multifocal enhancing tumefactive lesions on brain magnetic resonance imaging, and numerous small arteriolar ectasias on conventional angiography, with relapsing-remitting clinical features. KeyWords:Primary angiitis of the central nervous system, Magnetic resonance imaging, Small arteriolar ectasia