Dissociated Automatic-Voluntary Lower Cranial Nerve Palsies and Anarthria After Left Corona Radiata Infarction:Foix-Chavany-Marie Sydrome

J Korean Neurol Assoc > Volume 26(4); 2008 > Article

Journal of the Korean Neurological Association 2008;26(4): 357-360.

좌측 방사관 경색에 의해 발생한 자동-수의적 조절 해리를 보이는 하부 뇌신경마비와 조음불능증: Foix-Chavany-Marie증후군

김건하, 윤영신 김용재 김정은 박기덕 최경규 정지향

이화여자대학교 의과대학 신경과학교실, 이화여자대학교 의과대학 부속 목동병원

Dissociated Automatic-Voluntary Lower Cranial Nerve Palsies and Anarthria After Left Corona Radiata Infarction:Foix-Chavany-Marie Sydrome

Geon Ha Kim

Department of Neurology, Ewha Womans University School of medicine,Ewha Womans University Mokdong Hospital, Cognitive and Language Disorder clinic

Abstract

Foix-Chavany-Marie Syndrome (FCMS) is characterized by anarthria and bilateral facio-pharyngo-glosso-masticatory paralysis with an automatic-voluntary dissociation, which usually develops in bilateral opercular lesions. We present a case of FCMS caused by unilateral subcortical lesion. A 54-year-old man was admitted due to acute right hemiparesis with anarthria. He had voluntary facial paresis but automatic-involuntary facial movements were preserved. MRI showed an acute left corona radiata infarction and PET revealed decreased glucose metabolism in left basal ganglia and fronto-parietal lobe.