A Case of Limited Form of Wegener’s Granulomatosis Involving CNS

J Korean Neurol Assoc > Volume 24(6); 2006 > Article

Journal of the Korean Neurological Association 2006;24(6): 589-593.

중추신경계를 침범한 제한성 베게너 육아종증 1예

김성민, 김정민 김현정 김성헌 성정준 박경석a 홍윤호b

서울대학교 의과대학 신경과학교실, 서울대학교 의과대학 분당서울대학교병원 신경과a, 서울대학교 보라매병원 신경과a

A Case of Limited Form of Wegener’s Granulomatosis Involving CNS

Sung-Min Kim

Department of Neurology, Seoul National University College of Medicine, Seoul; Department of Neurology, Seoul National University Bundang Hospitala, Seongnam; Department of Neurology, Seoul National University Boramae Hospitalb, Seoul, Korea

Abstract

Wegener’s granulomatosis (WG) is a rare systemic necrotizing vasculitis, primarily affecting the upper and lower respiratory tracts, and kidney. Neurologic manifestations come later in one-third to one-half of cases, and usually take the forms of a peripheral neuropathy or multiple cranial neuropathies. Herein, we report a case with a “limited” form of WG which presented with cerebral and oculorhinal manifestations without renal and pulmonary involvement.KeyWords:Wegener’s granulomatosis, Vasculitis