A Case with Neuro-Sweet Syndrome

J Korean Neurol Assoc > Volume 23(5); 2005 > Article

Journal of the Korean Neurological Association 2005;23(5): 706-708.

Neuro-Sweet 증후군 1예

윤성희, 권석범 서희정 정 산 황성희 이병철

한림대학교 의과대학 신경과학교실

A Case with Neuro-Sweet Syndrome

Sung-Hee Yun

Department of Neurology, Hallym University College of Medicine, Seoul, Korea

Abstract

Sweet's syndrome, or acute febrile neutrophilic dermatosis, is an unusual disease characterized by fever, leukocytosis, and distinctive skin lesions. Common complications include arthralgia, arthritis, conjunctivitis, and iridocyclitis. However, the involvement of the central nervous system in this disease, termed 'neuro-Sweet syndrome' is rarely reported. We present a patient with recurrent encephalitis for 15 years, accompanied with neutrophilic dermatosis, and characterized by HLA-B54 and Cw1, with good responsiveness to corticosteroid.KeyWords:Sweet's syndrome, Behcet's disease, Neuro-Sweet syndrome