| Bilateral Anterior Opercular Syndrome 1예:
Foix-Chavany-Marie Syndrome |
| 김동억*, 이용석 ·박성호 ·박경일*·조중양*·김삼수†·남현우 ·이광우*·노재규* |
| 서울특별시립 보라매병원 신경과,방사선과†
서울대학교 의과대학 신경과학교실* |
| A Case of Bilateral Anterior Opercular Syndrome : Foix-Chavany-Marie Syndrome |
| Dong-Eog Kim, M.D.*, Yong-Seok Lee, M.D., Seong-Ho Park, M.D., Kyung-Il Park, M.D.*, Joong-Yang Cho, M.D.*, Sam Soo Kim, M.D.† Hyun-Woo Nam, M.D., Kwang-Woo Lee, M.D.*, Jae-Kyu Roh, M.D.* |
| Departments of Neurology and Radiology† , Seoul Municipal Boramae Hospital Department of Neurology, College of Medicine, Seoul National University* |
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| Abstract |
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Bilateral opercular syndrome or Foix-Chavany-Marie syndrome (FCMS) is characterized by facio-pharyngo-glosso-masticatory diplegia with an automatic-voluntary movement dissociation, which is usually caused by bilateral fron-toparietal opercular lesions. A 52 year-old man suddenly developed left hemiplegia and also presented with anarthria, dysphagia, difficulty in jaw opening and mastication. However, involuntary swallowing and slight control of jaw move-ments were partly preserved. His gag reflex was decreased and emotional incontinence was absent. Brain magnetic res-onance (MR) imaging revealed high signal lesions in the right middle cerebral artery territory and left anterior opercu-lum. Severe stenosis of the right middle cerebral artery was observed on a MR angiogram. Rehabilitation training by cueing has improved his ability to open the mouth. To our knowledge, this is the first report of FCMS in Korea, and a cautious differential diagnosis of pseudobulbar palsy or buccofacial apraxia may be crucial.
J Korean Neurol Assoc 18(4):450~453, 2000
Key Words : Bilateral anterior opercular syndrome, Foix-Chavany-Marie syndrome, Operculum, Automatic-voluntary dissociation |
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