| 특발성 비후성 두 개경막염 |
| 박지현, 김영인, 이광수, 김범생, 이상도, 손성일, 유영수, 임정근, 김상표 |
| 가톨릭대학교 의대 신경과, 계명대학교 의대 신경과. 병리학과 |
| Idiopathic hypertrophic cranial pachymeningitis : report of 2 cases & review of literatures |
| Ji Hyun Park, M.D., Yeong In Kim, M.D., Kwang Soo Lee, M.D., Beum Saeng Kim, M.D., Sang Doe Yi M.D., Sung Il Sohn, M.D., Young Soo Yoo, M.D., Jeong Geun Lim, M.D., Sang Pyo Kim, M.D. |
| Department of Neurology, Catholic University Medical College. Department of Neurology & Pathology, Keimyung University Medical College |
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| Abstract |
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Idiopathic hypertrophic cranial pachymeningitis(IHCP) is a rare chronic pro gressive fibrosing inflammation of pachymeninges of unknown origin. Since the spreading of CT and MRI, there has been a few cases of IHCP have been reported. We describe two patients of IHCP with brain parenchymal involvement presented as epilepsia partialis continua which has not been described as a symptom of IHCP and review the previous reported literatures. IHCP commonly presents headache, multiple cranial nerve palsy, ataxia, and sometimes seizure. In many cases, the CSF finding is noninfectious inflammation, and the erythrocyte sedimentation rate is elevated. The brain MRI is the best noninvasive tool for diagnosis of IHCP and shows diffuse thickening and enhancing dura, especially posterior fossa. IHCP responds steroid initially but recurs frequently and progresses chronically.
Key Words : Idiopathic hypertrophic cranial pachymeningitis, Epilepsia partialis continua |
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