A Case of Nonsystemic Vasculitic Neuropathy -Electrophysilogic and Pathologic Findings-

J Korean Neurol Assoc > Volume 14(4); 1996 > Article

Journal of the Korean Neurological Association 1996;14(4): 1018-1022.

비전신성 혈관염에 의한 말초 신경병증 1례 -전기생리 및 병리소견을 중심으로-

김춘식, 정근호 조필자 최병철 구혜수

국립의료원 신경과, 이화여자대학교 의과대학 병리과학교실

A Case of Nonsystemic Vasculitic Neuropathy -Electrophysilogic and Pathologic Findings-

Chun Sik Kim, M.D., Keun Ho Chung, M.D., Phil Za Cho, M.D., Byuong Cheol Choi, M.D., Hae Soo Koo, M.D.

Department of Neurology, National Medical Center, Department of Pathology, College of Medicine, Ewha Woman's University

Abstract

In nonsystemic vasculitic neuropathy, clinically only nerves are affected : there are no or few constitutional symptoms or serological abnormalities. The clinical and pathological features are those of an ischemic neuropathy caused by a necrotizing vasculitis of small arterioles. This is a case report of nonsystemic vasculitic neuropathy in a 22-year-old male who has the distal symmetric poIyneuropathy as a symptom of localized vsaculitis. The sural nerve biopsy showed a few myelin digestion chamber suggesting axonal degeneration. The patient was treated with steroid daily with gradual clinical and electorophysiological improvement.