2 Cases of Pathologically Proven Cephalic Fibromuscular Dysplasia

J Korean Neurol Assoc > Volume 13(1); 1995 > Article

Journal of the Korean Neurological Association 1995;13(1): 138-141.

조직생검으로 진단한 두부 섬유근성 이형성증 2례 보고

문태순, 하경식, 홍승희, 신동진, 박성혜

중앙 길 병원 신경과. 병리과

2 Cases of Pathologically Proven Cephalic Fibromuscular Dysplasia

Tae Sun Moon, M.D., Kyung Sik Ha, M.D., Seung Hee Hong, M.D., Dong Jin Shin, M.D., Sung Hye Park, M.D.

Department of Neurology, Pathology, Chung-Ang Gil Hospital

Abstract

Fibromuscular dysplasia (FMD) is a segmental nonatheromatous and noninflammatory angiopathy of unknown cause. Despite the unknown origin Of FMD, it has been recognized in the extracranial internal cartid, vertebral, and intracranial arteries. Usually the diagonsis of FMD has been done by angiographic findings, and pathologically proven cases are very rare. We report 2 patients who had suffered from hemicranial pain and ipsilateral ama-urosis figax, and whose initial laboratory evaluations revealed high ESR. The biopsy was done in the temporal artery under the impression of the temporal arteritis, which showed the findings of the fibromuscular dysplasia.