Repetitive Nerve Stimulation Test in Myotonic Patients

J Korean Neurol Assoc > Volume 12(4); 1994 > Article

Journal of the Korean Neurological Association 1994;12(4): 702-708.

근긴장증 환자에서의 반복신경자극검사 소견

박재현, 선우일남,문준식,이상암,박영관,김기환

인제대학교 신경과. 상계병원 신경과. 연세대학교 신경과.

Repetitive Nerve Stimulation Test in Myotonic Patients

Jae Hyeon Park, M.D., Il Nam Sunwoo, M.D., Joon Shik Moon, M.D., Sang Am Lee, M.D., Young Gwan Park, M.D., Ki Whan Kim, M.D.

Department of Neurology, College of Medicine, Inje University, Sanggye Paik Hospital, Department of Neurology, Yonsei University

Abstract

In 17 myotonic cases (16 of myotonic muscular dystrophy and 1 of congenital myotonia), 13 cases showed significant decremental responses on RNS study. The decremental responses had the tendency of more prominence on faster stimulating rate, and in the proximal limb muscles. This result suggests that the RNS test is useful but not specific for the disorder of neuromuscular junction.