A Case of EIEE(Early Infantile Epileptic Encephalopathy)

J Korean Neurol Assoc > Volume 11(3); 1993 > Article

Journal of the Korean Neurological Association 1993;11(3): 434-438.

조기 영아 간질성 뇌증 1례

조경원, 정원영,문경래,박상기,박영봉

조선대학교 신경과, 소아과.

A Case of EIEE(Early Infantile Epileptic Encephalopathy)

Kyung-Won Cho, M.D., Won-Young Jung, M.D., Kyeong-Rae Moon, M.D., Sang-Ki Park, M.D., Young-Bong Park, M.D.

Department of Neurology and Pediatrics, College of Medicine Chosun University

Abstract

The EIEE is defined by very early onest, within the first few months of life. Frequent tonic spasms, and suppression burst of EEG pattern in both waking and sleeping state. Its etiology and underlying pathology are obscure. The prognosis is usually grave with severe psychomotor retardation and intractable seizures. Occassionaly it may evolve into the West syndrome. We report a case of 3-month-old female delivered by Casesarean section, who showed typical features of EIEE disorder, with the review of literatures.