A Case of Wilson's Disease Associated with Somatomotor Status Epileticus

J Korean Neurol Assoc > Volume 9(3); 1991 > Article

Journal of the Korean Neurological Association 1991;9(3): 362-366.

체 운동 지속성 간질을 보인 윌슨씨 병 1예

정철, 박미영,변영주,박충서

영남대학교 신경과.

A Case of Wilson's Disease Associated with Somatomotor Status Epileticus

Cheoul Jung, M.D., Mee Yeong Park, M.D., Yeung Ju Byun, M.D., Choong Suh Park, M.D.

Dep. Of Neurology, Yeung Nam University

Abstract

Wilson's disease is a genetically transmitted autosomal recessive disorder of copper metabolism which affects the liver. Brain and other organs. The seizure in Wilson's disease is not infrequent but. It's report is very rare in Korea. The frequency of seizure is about 10 times more than that of general population The statistical proportions of types of seizure associated with Wilson's disease do not differ significantly from that seen in the general population. And the most common seizure type is focal motor form. The issue of the mechanisms producing seizure in Wilson's disease has attracted controversy, but the cause of seizure seems to be related with copper itself. Although the seizure is well controlled by anticonvulsants, the prognosis of seizure depends on the treatment of Wilson`s disease. We report a case of Wilson's disease associated with somatomotor status epilepticus.