A Case of Idiopathic Orbital Myositis

J Korean Neurol Assoc > Volume 6(1); 1988 > Article

Journal of the Korean Neurological Association 1988;6(1): 71-77.

비특이성 안와근염 1예

이종원, 김원천, 최일생, 유호민, 지제근

연세대학교 신경과, 안과. 서울대학교 신경병리학.

A Case of Idiopathic Orbital Myositis

Jong Won Lee, M.D., Won Tsen Kim, M.D., Il Saing Choi, M.D.,Ho Min Yoo, M.D

Department of Neurology, Yonsei University College of Medicine Department of Ophthalmology, Yonsei University College of Medicine Department of Neuropathology, Seoul University College of Medicine

Abstract

Idiopathic orbital myositis, a subgroup of previously so called inflammatory orbital pseudotumor, occurred with acute onset periorbital pain, eyelid swelling, proptosis, and ophthalmoplegia. Currently many pathologist and ophthalmologist agreed the term pseudotumor or Tolosa-Hunt syndrome and They classified some cases as characterized histologic and computerized tomographic evidence of inflammation of extraocular muscles, good responsiveness to prednisone, remission and exacerbation, with recurrence, but generally benign condition. The possibility of idiopathic orbital myositis being an immune-mediated process has been discussed. Some believe many of such cases have been grouped under the term Tolosa-Hunt syndrome. It is onloy in the last decade that computerized tomographic scanning has allowed precise localization of the alterations to orbital and retro-orbital strcutures. The term idopathic orbital myositis is precise insofar as it indicates the structures primarily involved ocular muscles. We report a case of idiopathic orbital myositis withr review of literatures.