A case of idiopathic exercise-induced axial dystonia with ipsilateral upper extremity      atrophy

J Korean Neurol Assoc > Volume 15(3); 1997 > Article

Journal of the Korean Neurological Association 1997;15(3): 691-694.

동측상지위축을 동반한 운동유발성 축성 근긴장이상 1례

이동국, 도진국, 곽규호, 오희종

대구 효성가톨릭대학교 의대 신경과

A case of idiopathic exercise-induced axial dystonia with ipsilateral upper extremity atrophy

Dong Kuck Lee, M.D., Jin Kuk Do, M.D., Kyu Ho Kwak, M.D., Hee Jong Oh, M.D.

Department of neurology, School of Medicine, Catholic University of Taegu-Hyosung

Abstract

Torsion dystonia (TD) is a clinical syndrome characterized by prolonged spasms of muscle contraction, which distort the body into typical dystonic posture. The pathological or biochemical basis of either the familial types or of most sporadic forms of idiopathic or primary TD is unknown. We present a 40-year old man who showed a kinesigenic axial dystonia with ipsilateral upper extremity atrophy for 14 years. The symptoms and signs were spontaneous onset, nonprogrwsive course, and induced by voluntary activity but relieved by rest and sleep and responded to trihexyphenidyl medication.