Progressive Moyamoya Syndrome Associated with Paroxysmal
Nocturnal Hemoglobinuria

J Korean Neurol Assoc > Volume 32(4); 2014 > Article

Journal of the Korean Neurological Association 2014;32(4): 285-288.

발작성야간혈색뇨증과 동반된 진행성 모야모야증후군

류성근, 이세진

영남대학교 의과대학 신경과학교실

Progressive Moyamoya Syndrome Associated with Paroxysmal Nocturnal Hemoglobinuria

Sung Geun Ryu

Department of Neurology, Yeungnam University College of Medicine, Daegu, Korea

Abstract

A 31-year-old female with paroxysmal nocturnal hemoglobinuria (PNH) presented with left hemiparesis. One year prior to this presentation she had been diagnosed with bihemispheric cerebral infarctions associated with moyamoya syndrome. During her current presentation, MRI revealed acute infarction of the right hemisphere and MRA revealed occlusion of the right internal carotid artery (ICA), and aggravation of the preexisting stenosis of the contralateral ICA and ipsilateral posterior cerebral artery compared to the previous MRA. We report herein a case of progressive moyamoya syndrome associated with PNH. Key Words: Moyamoya syndrome, Paroxysmal nocturnal hemoglobinuria, Progression