A Case of Adult-onset Rasmussen's Encephalitis Responsive to High-dose Steroid and Antiepileptic Medication

J Korean Neurol Assoc > Volume 22(1); 2004 > Article

Journal of the Korean Neurological Association 2004;22(1): 67-70.

고용량 스테로이드와 항경련제에 효과가 나타난 성인형 Rasmussen 뇌염 1예

이순금, 전민철 조광덕 임수빈

울산대학교 의과대학 강릉아산병원 신경과학교실, 서울아산병원 가정의학과학교실

A Case of Adult-onset Rasmussen's Encephalitis Responsive to High-dose Steroid and Antiepileptic Medication

Soon Keum Lee

Department of Neurology, Gangneung Asan Hospital; Department of Family Medicine, Asan Medical Center, University of Ulsan College of Medicine*, Seoul, Korea

Abstract

Rasmussen’s encephalitis is a rare autoimmune disorder characterized by intractable epilepsy and progressive unilateral hemispheric dysfunction as well as mental deterioration. Although the disorder typically begins in childhood, a few cases have been reported with symptom onset in adulthood showing variable clinical characteristics. We report a 63-year-old woman with adult-onset partial seizure with intermittent secondary generalization, progressive right hemiparesis, and aphasia, who showed positive response to high-dose steroid and antiepileptic drugs.Key Words: Rasmussen encephalitis, Steroid, Antiepileptic drugs