Two Cases of Evans Myopathy in a Family

J Korean Neurol Assoc > Volume 20(5); 2002 > Article

Journal of the Korean Neurological Association 2002;20(5): 568-570.

한 가족에서 발병한 Evans 근병증 2예

조정희 , 정연경 ·김승민 ·선우일남

연세대학교 의과대학 신경과

Two Cases of Evans Myopathy in a Family

Jung Hee Cho, M.D.

Departments of Neurology, Yonsei University College of Medicine

Abstract

"Evans myopathy is a type of malignant hyperthermia showing characteristic distribution of myopathic changes. We present two cases of Evans myopathy, father and his son in a family. Five members of this family expired during anes-thesia and surgery and two of these cases were reported as the malignant hyperthermia. The muscle pathology shows moth-eaten appearance with or without unstained cores in NADH-TR stain and its difference between the father and his son is suggestive of rather progressive myopathy than static one.Key Words : Evans myopathy, Malignant hyperthermia"

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