A Case of Fly Catcher’s Tongue Phenomenon in Hallervorden-Spatz Disease

J Korean Neurol Assoc > Volume 18(2); 2000 > Article

Journal of the Korean Neurological Association 2000;18(2): 255-257.

Fly Catcher ’s Tongue을 보인 Hallervorden-Spatz Disease

하충건, 강사윤 ㆍ나정호 ㆍ이일근

인하대학교 의과대학 신경과학교실

A Case of Fly Catcher’s Tongue Phenomenon in Hallervorden-Spatz Disease

Choong-Kun Ha, M.D., Sa-Yoon Kang, M.D., Joung-Ho Rha, M.D., Il-Keun Lee, M.D.

Department of Neurology, College of Medicine, Inha University

Abstract

Hallervorden-Spatz disease (HSD) is a rare, progressive, autosomal recessive hereditary disorder characterized by pyramidal and extrapyramidal signs, speech disturbances, mental deterioration and retinal degeneration during childhood or adolescence. In late-onset form after the age of 20, parkinsonian features may be the predominant clinical manifesta-tion. Meanwhile, involuntary tongue movements are rare and poorly understood, which have been reported in tardive dyskinesia, neuroacanthocytosis, chronic epilepsy, and after head trauma. We report a case of a patient with ‘fly catch-er’s tongue’ as a major clinical presentation, accompanied with mild parkinsonism, and typical MR findings of HSD. J Korean Neurol Assoc 18(2):255~257, 2000 Key Words : Fly catcher’s tongue, Hallervorden-Spatz disease Manuscript received October 6,1999.