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Journal of the Korean Neurological Association 1999;17(2): 285-288.
완전 기저 모야모야병(Moyamoya disease) 1례
권준범, 양현덕·한범기·이지용·문준식·이성수
연세대학교 원주의과대학 원주기독병원 신경과학교실
A Case of Moyamoya Disease Associated with Complete Duplication of the Basilar artery
Joon Bum Kwon, M.D., Hyun Duk Yang, M.D., Bum-Gi Han, M.D., Ji-Yong Lee, M.D., Joon-Shik Moon, M.D., Sung-Soo Lee, M.D.
Department of neurology, Wonju Christian Hospital, Wonju College of Medicine, Yonsei University
Abstract
Moyamoya disease is characterized by a bilateral progressive narrowing of the distal internal carotid and proximal portions of the anterior and middle cerebral arteries. The cerebral vessels of the 11 to 14 mm embryonic period are extremely similar to these moyamoya vessels. The vertebral arteries unite with a contralateral homologue to form the basilar artery during embryonic development and rarely, the failure of complete fusion results in duplication of these arteries. It is well known that moyamoya disease sometimes is accompanied by persistent primitive arteries, cerebral aneurysm, or rarely arteriovenous malformation. However, no case of the moyamoya disease with complete duplication of basilar artery has been previously reported. These two types of vascular abnormality are probably associated in certain developmental period, and moyamoya disease causes hemodynamic load in the basilar artery system as a collateral pathway and these effects are also involved in duplication of basilar artery. The relationship between these two varieties of vascular abnormality and possible pathogenesis of the moyamoya disease are discussed. Key Words : Moyamoya Disease, Complete Duplication of Basilar Artery, Pathogenesis