A case of temporal bone fibrous dysplasia causing central venous thrombosis and intracranial hypertension

J Korean Neurol Assoc > Volume 15(2); 1997 > Article

Journal of the Korean Neurological Association 1997;15(2): 448-453.

측두골 섬유성 이형성증에 속발된 중심정맥 폐쇄 및 두개내 고혈압증

홍경훈, 이영배, 이영주, 김희태, 김승현, 김주한, 김명호

한양대학교 의대 신경과

A case of temporal bone fibrous dysplasia causing central venous thrombosis and intracranial hypertension

Kyung Hoon Hong, M.D., Young Bae Lee, M.D., Young Ju Lee, M.D., Hee Tae Kim, M.D., Seung Hun Kim, M.D., Ju Han Kim, M.D., Myung-Ho Kim, M.D.

Department of Neurology College of Medicine Hanyang University

Abstract

Fibrous dysplasia is a slowly progressive benign fibro-osseous disorder of unknown cause. The predilection sites of the craniofacial bones are maxilia and mandible, but fibrous dysplasia of the temporal bone is rarely noted, The usual clinical manifestations of fibrous dysplasia of the temporal bone are mainly otologic complications such as progressive stenosis of the external auditory canal and conductive hearing loss. But its neurologic complications are very rarely reported except facial nerve paresis. We present a case of monostotic fibrous dysplasia of the temporal bone leading to intracranial hypertension with central venous thrombosis. To our knowledge, this association has not been previously described in the literature.