Isolated Angiitis of Cntral Nervous System ( A case Report)

J Korean Neurol Assoc > Volume 7(2); 1989 > Article

Journal of the Korean Neurological Association 1989;7(2): 373-376.

고립성 중추신경 혈관염 1례 보고

김종성, 서대철

울산대학교 신경과, 진단방사선과. 서울중앙병원 신경과, ?진단방사선과.

Isolated Angiitis of Cntral Nervous System ( A case Report)

Jong Sung Kim, M.D. Dae Chul Seo, M.D.

Department of Neurology, College of Medicine, University of Ulsan, Asan Medical Center Department of Diagnostic Radiology, College of Medicine, University of Ulsan, Asan Medical Center

Abstract

Isolated angiitis of central nervous system is a rare clinicopathologic entity characterized by vasculitis restricted to the vessels of the central nervous system without other apparent systemic vasculitis. We report a 57-year-old female patient who had suffered from repeated episodes of headache, vomiting and mental confusion. There was no evidence of systemic vasculitis. Brain CT scan showed multiple infarcts, and CSF showed mild pleocytosis and increased protein level. Cerebral angiogram confirmed the diagnosis by revealing multiple narrowing of small and medium sized arteries. Steroid and cyclophosphamide were tried with apparent benefit. Literatures are briefly reviewed.